Erdal Bodakçı, Mazhar Müslüm Tuna, Faruk Kılınç, zafer pekkolay, Hikmet Soylu, Alpaslan Tuzcu
Mazhar Müslüm Tuna, Dicle University Medical Faculty Endocrinology and Metabolism Division, Diyarbakır, Turkey Email: tunamazhar@gmail.com
ABSTRACT
McCune-Albright syndrome is characterized by polyostatic fibrous dysplasia, brown spots on the skin (café au lait pigmentation) and autonomous endocrine hyperfunction. Early puberty and other endocrinological manifestations, such as acromegaly, gigantism and hypercortisolism are widely observed in the syndrome. Acromegaly is seen in 20% of patients. We report a case of acromegaly accompanied with this syndrome.
Key words: McCune-Albright syndrome; acromegaly; fibrous dysplasia
Akromegalinin nadir bir nedeni: McCune-Albright sendromu
ÖZET
McCune-Albright sendromu, poliostotik fibröz displazi, deride kahverenginde lekelenme (Cafe au lait lekeleri) ve otonomik endokrin hiperfonksiyon ile karakterize bir sendromdur. Bu sendromda yaygın olarak erken puberte ve diğer endokrinolojik manifestasyonlar örneğin akromegali, jigantizm, hiperkortizolizm görülebilir. Akromegali Mc-Cune-Albriht sendromlu hastaların % 20 sinde görülebilir. Biz bu sendroma eşlik eden bir akromegali vakasını sunduk
Anahtar kelimeler: McCune-Albright sendromu, fibröz displazi, akromegali
Dicle Med J 2015;42(2):242-244
doi: 10.5798/diclemedj.0921.2015.02.0564
Volume 42, Number 2 (2015)
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