ISSN : 1300-2945
eISSN : 1308-9889
Abstract - A rare cause of acromegaly: McCune-Albright syndrome
Erdal Bodakçı, Mazhar Müslüm Tuna, Faruk Kılınç, zafer pekkolay, Hikmet Soylu, Alpaslan Tuzcu

Mazhar Müslüm Tuna, Dicle University Medical Faculty Endocrinology and Metabolism Division, Diyarbakır, Turkey Email: tunamazhar@gmail.com

ABSTRACT

McCune-Albright syndrome is characterized by polyostatic fibrous dysplasia, brown spots on the skin (café au lait pigmentation) and autonomous endocrine hyperfunction. Early puberty and other endocrinological manifestations, such as acromegaly, gigantism and hypercortisolism are widely observed in the syndrome. Acromegaly is seen in 20% of patients. We report a case of acromegaly accompanied with this syndrome.

Key words: McCune-Albright syndrome; acromegaly; fibrous dysplasia

Akromegalinin nadir bir nedeni: McCune-Albright sendromu

ÖZET

McCune-Albright sendromu, poliostotik fibröz displazi, deride kahverenginde lekelenme (Cafe au lait lekeleri) ve otonomik endokrin hiperfonksiyon ile karakterize bir sendromdur. Bu sendromda yaygın olarak erken puberte ve diğer endokrinolojik manifestasyonlar örneğin akromegali, jigantizm, hiperkortizolizm görülebilir. Akromegali Mc-Cune-Albriht sendromlu hastaların % 20 sinde görülebilir. Biz bu sendroma eşlik eden bir akromegali vakasını sunduk

Anahtar kelimeler: McCune-Albright sendromu, fibröz displazi, akromegali

Dicle Med J  2015;42(2):242-244

doi: 10.5798/diclemedj.0921.2015.02.0564

Volume 42, Number 2 (2015)